Mauriac syndrome is characterized by dwarfi sm, obesity
and hepatomegaly in patients with insulin-dependent
diabetes mellitus. It is associated with poor control of
type 1 diabetes mellitus (T1DM) in adolescents, and may
present as obesity, hepatomegaly, cushingoid facies and
elevated transaminases.[1] It is typically associated with
growth failure and delayed pubertal maturation, which
should alert the physician over insuffi cient management of
diabetes mellitus and the related development of Mauriac
syndrome, although these can be reversed with good
glycemic control.[2]